Papillomatosis Cutis Lymphostatica: A Comprehensive Guide To Diagnosis, Treatment, And Management
Papillomatosis cutis lymphostatica, a rare genetic syndrome caused by mutations in the FOXC2 gene, manifests as warty skin-colored papillomas and lymphedema, primarily affecting the lower extremities. Commonly appearing in infancy, it may be accompanied by facial dysmorphism, hearing loss, and intellectual disability. Diagnosis involves clinical evaluation and genetic testing, while treatment consists of surgical removal…